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Table 1 Patients’ diagnosis

From: Non-invasive quantification of pressure–volume loops in patients with Fontan circulation

Subject

Type of Fontan

Diagnosis

1

Extracardiac

HLHS

2

Extracardiac

HLHS, TAPVD

3

Extracardiac

Hypoplastic right PA, left isomerism, interrupted IVC

4

Extracardiac

Hypoplastic aortic arch, CoA, VSD, DORV

5

Extracardiac

DORV Taussig Bing, unbalanced AVSD, PS, TAPVD, right isomerism

6

Lateral tunnel

Single ventricle, DORV, TGA

7

Extracardiac

Single ventricle, PS, TGA, right isomerism, TAPVD

8

Extracardiac

TGA, multiple VSD:s, hypoplastic PA

9

Right atrium to PA

Tricuspid atresia

10

Extracardiac

DILV, TGA, PS

11

Lateral

Tricuspid atresia

12

Lateral

Tricuspid atresia

13

Extracardiac

HLHS

14

Extracardiac

DORV, TGA, multiple VSDs

15

Extracardiac

DIRV, TGA

16

Lateral

DORV

17

Extracardiac

HLHS

  1. NYHA New York Heart Association Functional Classification, HLHS Hypoplastic left heart syndrome, TAPVD Total Anomalous Pulmonary Venous Drainage, SVC superior vena cava, PA Pulmonary artery, IVC inferior vena cava, CoA Coarctatio of aorta, VSD ventricular septal defect, DORV Double outlet right ventricle, AVSD atrioventricular septal defect, PS pulmonary stenosis, TGA Transposition of the great arteries, DILV Double inlet left ventricle