Skip to main content

Table 1 Common complications of Eisenmenger syndrome. [3, 31, 32]

From: Eisenmenger syndrome with left main compression syndrome: a case report

No

Complications

Signs and symptoms

1

Secondary erythrocytosis

Hyperviscosity symptoms

2

Haemostasis abnormalities (increased risk in both bleeding and thrombosis)

Pulmonary bleeding (rupture of hypertrophied bronchial arteries)

Pulmonary embolism

Deep vein thrombosis (DVT)

Stroke or brain abscess

3

Arrhythmias

Ventricular arrhythmias (ventricular tachycardia [VT] or ventricular fibrillation [VF])

Supraventricular arrhythmias (atrial fibrillation [AF] or atrial flutter [Afl])

4

Endocarditis

Fever

5

Mechanical complications

Compression of LMCA

Chest pain (angina-like or not)

6

PA aneurysms, rupture and dissection

Acute dyspnoea on exertion

Haemodynamic decompensation

Sudden death

7

Compression of intrathoracic structures (recurrent laryngeal nerves)

Hoarseness

8

Cerebral hypoperfusion due to low cardiac output

Syncope

9

Renal dysfunction

Reduced urine output

Hyperuricaemia