Table 1 Characteristics of 89 reviewed cases of Berry syndrome
Variable (Number*) | n (%) |
|---|---|
Sex (73) | |
 Male | 49 (67.1%) |
Premature birth (28) | |
 Yes | 4 (14.3%) |
Presence of clinical symptoms | |
 Cyanosis (52) | 21 (40.4%) |
 Tachypnea/dyspnea/respiratory infection (52) | 31 (59.6%) |
 Cardiac murmur (52) | 23 (44.2%) |
 CHF/poor peripheral perfusion/tachycardia (52) | 15 (28.8%) |
 Poor feeding/lethargy/poor phonation/anuria (52) | 10 (19.2%) |
Age at diagnosis (81) | |
 Prenatal | 13 (16.0%) |
 ≤ 3 months | 43 (53.1%) |
 3 months-1 year | 13 (16.0%) |
 1–12 years | 5 (6.2%) |
 > 12 years | 2 (2.5%) |
 Autopsy | 5 (6.2%) |
Diagnostic methods (81) | |
 Cases used echocardiography | 67 (82.7%) |
Anomalies recognized by echocardiography (46) | |
 APW + AORPA + IAA/HAA/CoA | 28 (60.9%) |
 APW + IAA/HAA/CoA | 11 (23.9%) |
 Others | 7 (15.2%) |
AA morphology (89) | |
 IAA | 83 (93.3%) |
 CoA | 4 (4.5%) |
 HAA | 2 (2.2%) |
IAA types (76) | |
 A | 67 (88.2%) |
 B | 9 (11.8%) |
 C | 0 (0) |
APW types (71) | |
 I | 2 (2.8%) |
 II | 56 (78.9%) |
 III | 13 (18.3%) |
Types of ductus artery (77) | |
 Patent | 76 (98.7%) |
 Fibrous cord | 1 (1.3%) |
Types of PDA (31) | |
 Large | 20 (64.5%) |
 Constricting | 11 (35.5%) |
Original site of RPA (86) | |
 Type A (a straddling RPA) | 13 (15.1%) |
 Type B (a completely separated RPA) | 73 (84.9%) |
Associated cardiac and extracardiac anomalies (68) | |
 Yes | 11 (16.2%) |
Chromosomal abnormalities (14) | |
 Yes | 4 (28.6%) |
Age at surgery (62) | |
 ≤ 1 month | 31 (50.0%) |
 1–3 months | 12 (19.4%) |
 3 months-1 year | 14 (22.6%) |
 1–12 years | 4 (6.5%) |
 > 12 years | 1 (1.6%) |
Types of surgery (63) | |
 One-stage | 53 (84.1%) |
 Two-stage | 10 (15.9%) |
Postoperative complications | |
 Aortic arch stenosis (29) | 13 (44.8%) |
 RPA stenosis (29) | 17 (58.6%) |
 Residual APW (29) | 1 (3.4%) |
Reintervention after surgery (27) | |
 Yes | 13 (48.1%) |
Presence of massively dilated vascular sac (64) | |
 Yes | 5 (7.8%) |