ARVD/C (n = 155) | ARVD/C ECG-positive (N = 84) | ARVD/C ECG-negative (N = 66) | P-value ECG positive/ negative | |
---|---|---|---|---|
ECG: Depolarization | ||||
- Epsilon waves | 13 (8.4%) | 13 (15.5%) | 0 (0.0%) | <0.001 |
- upslope S-wave ≥55 ms V1,V2 or V3 | 17 (11.0%) | 17 (20.2%) | 0 (0.0%) | <0.001 |
Bundle branch blocks | 22 (14.1%) | 17 (20.2%) | 0 (0.0%) | 0.035 |
SAECG performed (% total) | 63 (40.7%) | 32 (38.1%) | 31 (41.7%) | 0.515 |
- fQRSd ≥114 ms (% of SAECG) | 33 (52.4%) | 17 (53.1%) | 16 (51.6%) | 1.000 |
- LAS40 ≥ 38 ms (% of SAECG) | 31 (49.2%) | 18 (56.3%) | 13 (41.9%) | 0.317 |
- RMS40 ≤ 20 μV (% of SAECG) | 28 (44.4%) | 13 (40.6%) | 15 (48.4%) | 0.616 |
ECG: Repolarization | ||||
- T-wave inversions V1-V3 > 14 years no RBBB | 54 (34.8%) | 54 (64.3%) | 0 (0.0%) | <0.001 |
- T-wave inversions V1-V4 with RBBB | 12 (7.7%) | 12 (14.3%) | 0 (0.0%) | <0.001 |
- T-wave inversions V1 and V2 or in V4,V5,V6 | 8 (5.2%) | 8 (9.5%) | 0 (0.0%) | 0.008 |
Imaging | ||||
Echocardiograms performed (% total) | 155 (100.0%) | 84 (100.0%) | 66 (100.0%) | 1.000 |
- Regional akinesia/dyskinesia/aneurysm (% echo) | 111 (71.6%) | 65 (77.4%) | 43 (65.2%) | 0.108 |
MRI’s performed (% total) | 124 (80.0%) | 72 (85.7%) | 52 (73.2%) | 0.070 |
- Regional akinesia/dyskinesia/aneurysm (% MRI) | 89 (71.8%) | 58 (80.6%) | 31 (59.6%) | 0.272 |
- RVEDV ≥110 ml/m2 (M), 100 ml/m2 (F) (%MRI) | 65 (52.4%) | 49 (68.1%) | 16 (30.8%) | <0.001 |
- RVEDV ≥100 ml/m2 but <110 ml/m2 (M), ≥90 ml/m2 but <100 ml/m2 (F) (%MRI) | 24 (19.4%) | 10 (11.9%) | 14 (26.9%) | 0.106 |