Ambrisentan (N = 133) | |
---|---|
Age, years, mean (SD) | 36 (10.3) |
Gender, n (%) | |
Men/women | 20 (15)/113 (85) |
Ethnicity, n (%) | |
Not Hispanic or Latino ethnicity | 133 (100) |
BMI (kg/m2), mean (SD) | 21.5 (3.2) |
PAH classification, n (%) | |
PAH associated with connective tissue disease | 71 (53.4) |
Idiopathic PAH | 47 (35.3) |
PAH associated with congenital heart disease | 12 (9.0) |
Heritable PAH | 3 (2.3) |
6MWD, m, mean (SD) | 377.1 (61.3) |
WHO PAH functional classification, n (%) | |
Class II | 70 (52.6) |
Class III | 63 (47.4) |
BDI, mean (SD) | 2.5 (1.4) |
NT-ProBNP (ng/L), mean (SD) | 1600.7 (1832.84) |