Table 2 Blood test data

vWF antigen (IU/dL)

137 ± 14.5

147 ± 11.7

50–200

0.611

vWF activity (IU/dL)

90 ± 11

132.6 ± 13

50–200

0.017

[vWF activity]/[vWF antigen] ratio

0.65 ± 0.02

0.92 ± 0.06

>0.60

0.001

ADAMTS13 (%)

80.3 ± 4.7

96.2 ± 3.5

>40

0.016

Factor VIII (%)

173 ± 16

167.4 ± 16

55–205

0.813

Fibrinogen (mg/dL)

408.4 ± 23.4

371 ± 23.2

160–400

0.272

D-dimers (ng/mL FEU)

3217.7 ± 735

680.6 ± 223.2

<500

0.006

vWF multimer deficit levels

3/15

1/12

NA

0.396

Blood group “O” (% of patients)

33

41

NA

0.683

Platelet count (10⁹/L)

237 ± 25

207 ± 20

150–450

0.373

INR

2.6 ± 0.2

1.4 ± 0.2

0.8–1.2

0.001

aPTT (sec)

34.4 ± 1.2

26.5 ± 1.3

24–35

0.001

PT (%)

28.8 ± 3.5

78.2 ± 9.8

70–130 %

0.001

CRP

14.1 ± 3.8

6.45 ± 2

<10

0.108

Bilirubin total

0.58 ± 0.07

0.68 ± 0.1

<1.2

0.448

Alkaline Phosphatase

95.3 ± 15.2

77.7 ± 11.6

56–119

0.383

ALT (SGPT)

23.3 ± 3.85

56 ± 21.8

<45

0.113

AST (SGOT)

21.4 ± 1.35

47.4 ± 19.4

<35

0.146

Multiplate analysis

 Ristocetin 1 mg/mL (U)

61 ± 8.2

92.6 ± 9.7

90–201

0.019

 Adenosine diphosphate (U)

62.3 ± 6.3

73.7 ± 8.7

53–122

0.285

 Thrombin receptor activating peptide-6 (U)

93.7 ± 5.6

113.8 ± 6.5

94–156

0.028

 Arachidonic acid (U)

33.1 ± 7.6

60.7 ± 8.5

75–136

0.024

 Collagen binding activity assay (U)

43.1 ± 4.6

62.8 ± 5.8

46–117

0.012

 Spontaneous (U)

10 ± 2.3

14.3 ± 2.5

1–25

0.226