Myocardial lipid content in Fabry disease: a combined 1H-MR spectroscopy and MR imaging study at 3 Tesla

Table 1 Clinical and laboratory characteristics of the patients group (n = 30)

Patient	age [years]	gender	BMI [kg/m2]	SBP [mmHg]	DBP [mmHg]	ERT [years]	GFR [ml/min]	Crea. [mg/dl]	EF [%]	LVM [g]	LGE	lipids [%]	NS
1	49	f	33.8	140	100	0	113	0.6	55	92	y	0.27	n
2	43	f	20.6	125	60	0	116	0.6	64	127	y	3.29	y
3	17	m	20.0	138	73	1	156	0.7	56	131	n	0.15	y
4	52	f	23.5	170	70	7	82	0.8	70	197	y	5.14	y
5	23	m	29.2	120	78	4	127	0.8	64	217	n	1.76	n
6	43	m	28.7	125	83	9	47	1.7	71	207	y	0.10	y
7	50	f	23.3	104	69	3	70	0.9	78	161	y	0.14	n
8	37	f	27.3	115	85	0	120	0.6	59	104	n	0.30	n
9	51	f	21.6	101	74	3.5	80	0.8	69	78	y	1.36	n
10	19	m	20.2	108	88	3.5	116	0.9	53	129	n	0.61	n
11	27	f	20.5	115	80	0	91	0.8	65	88	n	4.05	n
12	50	f	37.7	178	88	9	94	0.7	79	189	y	0.92	y
13	52	f	38.7	145	95	9	93	0.7	83	175	y	0.85	y
14	43	m	19.2	120	70	10	47	1.7	60	227	y	0.54	y
15	53	f	22.8	120	80	4	76	0.8	73	132	y	0.22	n
16	50	m	17.5	110	80	7	95	0.9	69	253	y	0.30	y
17	42	m	26.9	140	85	7	95	0.9	47	386	y	0.24	y
18	48	f	23.1	110	75	0	86	0.8	69	192	n	0.23	n
19	17	f	19.4	108	76	0	---	0.8	56	83	y	3.59	n
20	68	f	19.8	115	80	0	82	0.7	66	84	n	0.90	y
21	46	m	25.4	129	70	9	69	1.2	65	226	y	0.14	y
22	28	m	31.0	115	65	6	158	0.6	57	155	y	0.10	y
23	50	f	27.2	112	104	0	71	0.9	68	141	y	0.57	n
24	30	m	24.3	135	90	4	112	0.9	69	176	y	0.45	y
25	42	m	21.0	155	95	6	96	0.9	52	179	y	0.10	y
26	22	f	19.3	116	67	0	111	0.7	69	73	n	0.10	n
27	61	f	18.9	140	66	0	77	0.8	61	87	n	0.70	y
28	51	f	21.4	91	69	0	70	0.9	69	140	y	0.18	n
29	51	f	28.4	145	95	0	69	0.9	56	148	y	0.16	y
30	28	m	24.2	133	70	9	90	1.0	55	203	n	0.36	n

BMI body mass index, SBP systolic blood pressure, DBP diastolic blood pressure, ERT treatment with enzyme replacement therapy, GFR glomerular filtration rate, Crea serum creatinine concentration, EF ejection fraction, LVM left ventricular mass, LGE late enhancement, NS neurological symptoms

ISSN: 1471-2261