From: Long-term results of treatment with bosentan in adult Eisenmenger’s syndrome patients with Down’s syndrome related to congenital heart disease
Parameter
Baseline
Final follow-up
P valuea
RVSP from TR (mmHg) (n = 4)
94.0 ± 13.4
85.5 ± 7.6
0.3750
Peak velocity of PR (m/s) (n = 2)
4.00 ± 0.14
4.05 ± 0.07
1.0000
AcT (m/s)
62.9 ± 11.6
83.0 ± 9.6
0.0156
AcT/ET
0.24 ± 0.04
0.30 ± 0.02