Case no. | Case 1 | case 2 | Case 3 | case 4 | Case 5 | Case 6 | Case 7 | Case 8 | Case 9 | Case 10 |
---|---|---|---|---|---|---|---|---|---|---|
Sex | male | female | female | male | female | female | female | male | female | male |
Age | 67 | 93 | 72 | 66 | 56 | 84 | 74 | 67 | 64 | 63 |
Cardiovascular disorder | Abdominal aortic aneurysm | Aortic dissection (type A) | Aortic dissection (type A) | Thoracic aortic aneurysm | Abdominal aortic aneurysm | Aortic stenosis | Aortic stenosis + regurgitation | Aortic stenosis + regurgitation | Aortic stenosis | Aortic stenosis |
Tissue sampled | aortic wall | aortic wall | aortic wall | aortic wall | aortic wall | aortic valve | aortic valve | aortic valve | aortic valve | aortic valve |
IgG4 (/HPF) | 101 | 18.7 | 35 | 37.5 | 5.2 | 73 | 3 | 20 | 3 | 23.5 |
IgG4/IgG (CD138) ratio (%) | 75 | 41.3 | 46.7 | 51.3 | 12.4 | 44.8a | 8a | 17.4a | 30a | 31.5a |
Obliterating phlebitis | + | - | - | - | - | - | - | - | - | - |
Storiform fibrosis | + | - | - | + | - | - | - | - | - | - |
Lymphoid follicle | + | - | - | + | + | - | - | - | - | - |
Eosinophil infiltration | + | - | - | - | - | - | - | - | - | - |
Neutrophil infiltration | - | + | - | - | - | - | - | - | - | - |
Perineural inflammation | + | - | - | - | - | - | - | - | - | - |
Granuloma | - | - | - | - | - | - | - | - | - | - |
Thickness of adventitial fibrosis, mm | 2.4 | 1 | 2 | 1.2 | 0.1 | N/A | N/A | N/A | N/A | N/A |
Hemosiderin deposition | - | + | + | - | + | + | + | - | - | + |